From: Medium-chain Acyl-CoA dehydrogenase deficiency presenting with neonatal pulmonary haemorrhage
Variable | At referral from other hospital, Day 2 | On admission to this hospital, Day 2 | Day 3 | Day 12 | Normal range |
---|---|---|---|---|---|
C-reactive protein (mg/dl) | <0.1 | <0.5 | <0.5 | <0.5 | |
Haematocrit (%) | 42.8 | 33 | 42 | 42 - 60 | |
Haemoglobin (g/dl) | 16.3 | 11.5 | 14.6 | 13,5 - 20,5 | |
Mean corpuscular volume (μm3) | 92 | 105.4 | 102.8 | 88 - 104 | |
White-cell count (per mm3) | 18.4 | 16.8 | 13.5 | 6.0 - 17.5 | |
Platelet count (per mm3) | 234000 | 220000 | 183000 | 140,000 - 440,000 | |
Prothrombin time (%) | 27 | 51 | 79 | 60 - 100 | |
International normalised ratio | 2.64 | 1.58 | 1.04 | ||
Partial-thromboplastin time (sec) | 131* | 30 | 35 | 22 - 38 | |
Fibrinogen (mg/dl) | 99 | 113 | 391 | 160 - 415 | |
Sodium (mmol/l) | 143 | 134 | 139 | 132 - 146 | |
Potassium (mmol/l) | 4.67 | 4.2 | 4.63 | 3,5 - 5,0 | |
Chloride (mmol/l) | 106 | 103 | 94 - 110 | ||
Bicarbonate (mmol/l) | 16 | 22 | 22 - 29 | ||
Calcium (mEq/l) | 4.2 | 5.3 | 4.3 - 5.1 | ||
Glucose (mg/dl) | 24 | 167 | 163 | 79 | 70 - 115 |
Creatinine (mg/dl) | 0.85 | 0.39 | 0.24 - 0.85 | ||
Total bilirubin (mg/dl) | 5.31 | 15.6 | 1.50 - 12.00 | ||
Protein (g/dl) | 4.4 | 5 | 5.6 | 4.6 - 6.8 | |
Albumin (g/dl) | 3.5 | 3.6 | 4 | 2.8 - 4.4 | |
Alanine aminotransferase (U/l) | 29 | 34 | <41 | ||
Aspartate aminotransferase (U/l) | 59 | 88 | <37 | ||
Lactate dehydrogenase (U/l) | 1040 | 240 - 480 | |||
Creatine kinase (U/l) | 1658 | <652 | |||
Blood gas analysis | |||||
pH | 7.26 | 7.351 | 7.115 | 7.35 - 7.45 | |
pO2 (mmHg) | 147 | 74.9 | 83 - 108 | ||
pCO2 (mmHg) | 33.2 | 72.7 | 35 - 48 | ||
Actual base excess (mmol/l) | -6.4 | -8.6 | -2.0 - +3.0 | ||
Lactate (mmol/l) | 1.8 | 1.4 | 0.5 - 1.6 |